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STUDIO ECOGRAFICO DOTT. IGNAZIO INDORATO

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339/6649270

https://pubmed.ncbi.nlm.nih.gov/33084435/

Diffuse cerebral angiomatosis associated to basilar apex aneurysm

 

Giuseppe Emmanuele Umana, Angelo Spitaleri, Marco Fricia, Ignazio Indorato, Giovanni Federico Nicoletti, Salvatore Cicero, Gianluca Scalia

Affiliations expand

PMID: 33084435

 

DOI: 10.1080/02688697.2020.1836324

Abstract

Background: Diffuse cerebral angiomatosis (DCA) is a diffuse infiltration of normal brain by complex vascular structures. It differs from arteriovenous malformations (AVMs) that are composed of a nidus of vessels through which arteriovenous shunting occurs without interposed functional brain parenchyma. A rare subgroup of AVMs is diffuse with no recognizable nidus with functional neuronal tissue interspersed within the malformed vessels. We present a rare association of DCA and cerebral arterial aneurysm, which dramatically influenced the patient's prognosis.

Case description: A 43-year-old male patient with right hemispheric diffuse cerebral angiomatosis presented with a ruptured basilar tip aneurysm that was successfully embolised. Unfortunately, the patient developed a locked-in syndrome.

Conclusion: The present report shows a possible association between diffuse cerebral angiomatosis and cerebral aneurysms, but this association appears to be less strong than it is with other AVMs.

Keywords: Diffuse cerebral angiomatosis; aneurysm; angiography; hemispheric vascular malformation; proliferative cerebral angiopathy; subarachnoid hemorrhage.